| 已发布 PubMed:高十六酸水平与冠心病有关。 High hexacosanoic acid levels are associated with coronary artery disease. |
| 已发布 PubMed:高十六酸水平与冠心病有关。 High hexacosanoic acid levels are associated with coronary artery disease. |
| 已发布 PubMed:减少多发性硬化症灰质中橙花元过氧化物酶体。 Reductions in neuronal peroxisomes in multiple sclerosis grey matter. |
| 已发布 PubMed:新黄烷和烷基α New flavan and alkyl alpha,霍斯菲尔德氏菌茎皮中的β-内酯。 beta-lactones from the stem bark of Horsfieldia superba. |
| 已发布 PubMed:电喷雾电离质谱法筛选正在发育的栽培花生和野生花生仁（花生）中的三酰基甘油。 An electrospray ionisation-mass spectrometry screening of triacylglycerols in developing cultivated and wild peanut kernels (Arachis hypogaea L.). |
| 已发布 PubMed:zellweger综合征-一种致命的过氧化物酶体生物发生障碍。 Zellweger syndrome - a lethal peroxisome biogenesis disorder. |
| 已发布 PubMed:粘菌纲粘虫种的种子的脂肪油的化学组成。 Chemical composition of the fatty oils of the seeds of Cleome viscosa accessions. |
| 已发布 PubMed:拟南芥9参与角质层形成和维持植物水分状况。 Arabidopsis ECERIFERUM9 involvement in cuticle formation and maintenance of plant water status. |
| 已发布 PubMed:骨髓移植对x-连锁肾上腺白质营养不良的氧化应激的影响。 The effect of bone marrow transplantation on oxidative stress in X-linked adrenoleukodystrophy. |
| 已发布 PubMed:酰基-Coa氧化酶1缺乏症（假性新生儿肾上腺皮质营养不良）的炎症反应。 The inflammatory response in acyl-CoA oxidase 1 deficiency (pseudoneonatal adrenoleukodystrophy). |
| 已发布 PubMed:苯扎贝特通过抑制脂肪酸延伸降低了X链肾上腺皮质营养不良的成纤维细胞中的长链脂肪酸。 Bezafibrate lowers very long-chain fatty acids in X-linked adrenoleukodystrophy fibroblasts by inhibiting fatty acid elongation. |
| 已发布 PubMed:甲氟哌啶和全氟啶酮对饱和超长链脂肪酸生物合成的抑制作用 Inhibition of saturated very-long-chain fatty acid biosynthesis by mefluidide and perfluidone, 3-酮酰基-Coa合酶的选择性抑制剂。 selective inhibitors of 3-ketoacyl-CoA synthases. |
| 已发布 PubMed:油性混合物 A mixture of oleic, 使用电膜萃取与分散液-液微萃取相结合的气相色谱法从 尿中提取吡啶衍生物。 erucic and conjugated linoleic acids modulates cerebrospinal fluid inflammatory markers and improve somatosensorial evoked potential in X-linked adrenoleukodystrophy female carriers. |
| 已发布 PubMed:肾上腺皮质营养不良/肾上腺皮质橙花病亚临床肾上腺衰竭可逆吗？ Is subclinical adrenal failure in adrenoleukodystrophy/adrenomyeloneuropathy reversible? |
| 已发布 PubMed:西伯利亚 参的活性成分用于保护淀粉样β（25-35）诱导的大鼠皮质橙花元橙花营养性萎缩。 Active components from Siberian ginseng (Eleutherococcus senticosus) for protection of amyloid β(25-35)-induced neuritic atrophy in cultured rat cortical neurons. |
| 已发布 PubMed:多壁碳纳米管表面辅助激光解吸/电离质谱法测定 血浆中超长链脂肪酸方法 Screening assay of very long chain fatty acids in human plasma with multiwalled carbon nanotube-based surface-assisted laser desorption/ionization mass spectrometry. |
| 已发布 PubMed:姜根茎的化学成分 [Chemical constituents of rhizomes of Zingiber officinale]. |
| 已发布 PubMed:柑桔果皮的植物化学研究。 Phytochemical investigation of the fruit peels of Citrus reticulata Blanco. |
| 已发布 PubMed:丙戊酸在X连锁肾上腺皮质营养不良中诱导抗氧化作用。 Valproic acid induces antioxidant effects in X-linked adrenoleukodystrophy. |
| 已发布 PubMed:洛伐他汀在x连锁的肾上腺白质营养不良中。 Lovastatin in X-linked adrenoleukodystrophy. |
| 已发布 PubMed:中子衍射法研究具有游离脂肪酸成分的角质层脂质模型膜 Investigation of stratum corneum lipid model membranes with free fatty acid composition by neutron diffraction. |
| 已发布 PubMed:被诊断为多发性硬化症的患者的长链脂肪酸水平很高。 Very long chain fatty acid levels in patients diagnosed with multiple sclerosis. |
| 已发布 PubMed:超长链饱和脂肪酸在双层膜上的快速扩散以及环糊精的快速提取 Fast diffusion of very long chain saturated fatty acids across a bilayer membrane and their rapid extraction by cyclodextrins: 对肾上腺白质营养不良的影响。 implications for adrenoleukodystrophy. |
| 已发布 PubMed:一种基于热辅助水解和甲基化的气相色谱-质谱法快速鉴定痰液和培养物中结核分枝杆菌的方法。 A fast method for the identification of Mycobacterium tuberculosis in sputum and cultures based on thermally assisted hydrolysis and methylation followed by gas chromatography-mass spectrometry. |
| 已发布 PubMed:微型榕树气生根化学成分的研究 [Studies on chemical constituents of aerial roots of Ficus microcarpa]. |
| 已发布 PubMed:来自微生物的奇数个超长链脂肪酸 Odd-numbered very-long-chain fatty acids from the microbial, 动植物王国。 animal and plant kingdoms. |
| 已发布 PubMed:X连锁肾上腺白质营养不良 X-linked adrenoleukodystrophy: 巴西南部的临床病程和最低发病率。 clinical course and minimal incidence in South Brazil. |
| 已发布 PubMed:表皮脂质诱导恰加斯病载体中的聚集。 Epicuticular lipids induce aggregation in Chagas disease vectors. |
| 已发布 PubMed:全血中超长链脂肪酸浓度与儿童心血管危险因素有关。 Concentrations of very long-chain fatty acid in whole blood are associated with cardiovascular risk factors in children. |
| 已发布 PubMed:缩醛磷脂参与非常长链脂肪酸诱导的病理。 Plasmalogens participate in very-long-chain fatty acid-induced pathology. |
| 已发布 PubMed:过氧化物酶体abcd2转运蛋白在脂肪酸稳态中的关键作用。 A key role for the peroxisomal ABCD2 transporter in fatty acid homeostasis. |
| 已发布 PubMed:X肾上腺皮质营养不良中橙花退行性变的早期氧化损伤。 Early oxidative damage underlying neurodegeneration in X-adrenoleukodystrophy. |
| 已发布 PubMed:一种简单灵敏的液相色谱法，用于分析游离二十烷酸 A simple and sensitive liquid chromatographic method for the analysis of free docosanoic, 血浆中的十四烷酸和十六烷酸作为荧光衍生物。 tetracosanoic and hexacosanoic acids in human plasma as fluorescent derivatives. |
| 已发布 PubMed:高含量的饱和超长链脂肪酸（己酸； c26 High levels of saturated very long-chain fatty acid (hexacosanoic acid; C26:0）全血与日本男性的代谢综合症有关。 0) in whole blood are associated with metabolic syndrome in Japanese men. |
| 已发布 PubMed:角质层模型膜中的脂肪酸叉指 Fatty acid interdigitation in stratum corneum model membranes: 中子衍射研究。 a neutron diffraction study. |
| 已发布 PubMed:rnai介导的大鼠c6胶质细胞中abcd3基因表达的沉默 RNAi-mediated silencing of ABCD3 gene expression in rat C6 glial cells: 研究pmp70功能的模型系统。 a model system to study PMP70 function. |
| 已发布 PubMed:滇杂草化学成分的研究 [Studies on chemical constituents of Heterosmilax yunnanensis]. |
| 已发布 PubMed:患有儿童期和无症状x连锁性肾上腺橙花营养不良的患者的血浆中的十六烷酸和二十二烷酸水平 Hexacosanoic and docosanoic acids plasma levels in patients with cerebral childhood and asymptomatic X-linked adrenoleukodystrophy: Lorenzo'soil 影响 effect. |
| 已发布 PubMed: lespedeza cuneata中的新黄酮和其他成分。 |
| 已发布 PubMed:脂肪酸合酶的下调增加了酿酒酵母细胞对h2o2的抗性。 Down-regulation of fatty acid synthase increases the resistance of Saccharomyces cerevisiae cells to H2O2. |
| 已发布 PubMed:症状和无症状的x连锁性肾上腺橙花营养不良患者的脂质过氧化诱导诱导作用和抗氧化防御能力降低。 Induction of lipid peroxidation and decrease of antioxidant defenses in symptomatic and asymptomatic patients with X-linked adrenoleukodystrophy. |
| 已发布 PubMed:新型隐球菌糖苷醇磷酰基橙花酰胺结构突变株的表征。 Characterization of glycoinositolphosphoryl ceramide structure mutant strains of Cryptococcus neoformans. |
| 已发布 PubMed: 新型的游离橙花酰胺，作为台湾地下白蚁（coptotermes formosanus formosanus）的士兵防御腺的成分。 |
| 已发布 PubMed: 从kadsura 榆绿木 ananosma具有dna裂解活性的化合物。 |
| 已发布 PubMed:液相色谱-串联质谱联用作为高通量筛选x连锁肾上腺皮质营养不良和其他过氧化物酶体异常的分析方法 Combined liquid chromatography-tandem mass spectrometry as an analytical method for high throughput screening for X-linked adrenoleukodystrophy and other peroxisomal disorders: 初步发现。 preliminary findings. |
| 已发布 PubMed:The 影响 effect of Lorenzo'soil on 氧化 oxidative 强调 stress in X连锁肾上腺白质营养不良 X-linked adrenoleukodystrophy. |
| 已发布 PubMed:跟进 Follow-up of 89 无症状的 a有症状的 symptomatic 耐心 patients with 肾上腺白质营养不良 adrenoleukodystrophy 处理过的 treated with Lorenzo'soil. |
| 已发布 PubMed:一种新颖的同轴电喷雾电离方法，用于通过傅里叶变换离子回旋共振质谱法表征十六烷酰基橙花酰胺。 A novel coaxial electrospray ionization method for characterizing hexacosanoylceramides by Fourier transform ion cyclotron resonance mass spectrometry. |
| 已发布 PubMed:[关于鸡血藤茎的成分的研究]。 [Studies on the constituents from the stems of Spatholobus suberectus]. |
| 已发布 PubMed:非常长的链脂肪酸会激活 皮肤成纤维细胞中的纳德氧化酶。 Very long chain fatty acids activate NADPH oxidase in human dermal fibroblasts. |
| 已发布 PubMed:圭亚那锦葵的成分（mel科）。 Constituents of Carapa guianensis Aubl. (Meliaceae). |
| 已发布 PubMed:中草药十二指肠化学成分的研究 [Studies on the chemical constituents of Chinese herb Melastoma dodecandrum]. |
| 已发布 PubMed:hplc-ms方法，使用部分可混溶的溶剂分析十八烷基硅胶相上的长链脂肪酸和其他非极性化合物。 An HPLC-MS approach for analysis of very long chain fatty acids and other apolar compounds on octadecyl-silica phase using partly miscible solvents. |
| 已发布 PubMed:有证据表明，x连锁肾上腺皮质营养不良患者的氧化应激增加。 Evidence that oxidative stress is increased in patients with X-linked adrenoleukodystrophy. |
| 已发布 PubMed:富含己酸c6橙花胶质细胞中的自由基释放 Free radical release in C6 glial cells enriched in hexacosanoic acid: 提示x连锁性肾上腺白质营养不良的发病机制。 implication for X-linked adrenoleukodystrophy pathogenesis. |
| 已发布 PubMed:毛滴虫滴眼液中萜类化合物的抗菌活性。 Antimicrobial activity of terpenoids from Trichodesma amplexicaule Roth. |
| 已发布 PubMed:[紫锥菊的脂质化合物]。 [Lipid compounds from Echinacea purpurea]. |
| 已发布 PubMed: [花椒化学成分的研究。 var 刺叶 spinifolium rhed。等）。 |
| 已发布 PubMed:麻黄化学成分的研究 [Studies on the chemical constituent of Ephedra likiangensis]. |
| 已发布 PubMed:[x连锁肾上腺皮质营养不良的临床异质性]。 [Clinical heterogeneity of X-linked adrenoleukodystrophy ]. |
| 已发布 PubMed:X联肾上腺白质营养不良患者血浆中超长链脂肪酸诊断模式。 Diagnostic patterns of very-long-chain fatty acids in plasma of patients with X-linked adrenoleukodystrophy. |
| 已发布 PubMed:血红细胞膜中十六烷酸酯水平升高与动脉粥样硬化危险因素的相关性。 Correlations of elevated levels of hexacosanoate in erythrocyte membranes with risk factors for atherosclerosis. |
| 已发布 PubMed:患者体内的睾丸激素代谢物会降低x-肾上腺白质营养型成纤维细胞中积累的非常长链脂肪酸水平。 Testosterone metabolites in patients reduce the levels of very long chain fatty acids accumulated in X-adrenoleukodystrophic fibroblasts. |
| 已发布 PubMed:洛伐他汀治疗x连锁性肾上腺白质营养不良 Lovastatin therapy for X-linked adrenoleukodystrophy: 12例患者的临床和生化观察。 clinical and biochemical observations on 12 patients. |
| 已发布 PubMed:是增味剂鸟苷一磷酸（gmp）的二钠盐。鸟苷酸二钠是食品添加剂，通常与谷氨酸（谷氨酸钠）结合使用 Inactivation of the inhA-encoded fatty acid synthase II (FASII) enoyl-acyl carrier protein reductase induces accumulation of the FASI end products and cell lysis of Mycobacterium smegmatis. |
| 已发布 PubMed:哺乳动物新基因家族在长链脂肪酸和鞘脂的生物合成中的作用 Role of a new mammalian gene family in the biosynthesis of very long chain fatty acids and sphingolipids. |
| 已发布 PubMed:进展 Progression of 异常 异常 ab正常 normalities in 肾上腺橙花病 adrenomyeloneuropathy and 橙花学上 橙花学的 neurologically 无症状的 a有症状的 symptomatic X连锁肾上腺白质营养不良 X-linked adrenoleukodystrophy 尽管 despite 治疗 treatment with "Lorenzo'soil". |
| 已发布 PubMed:rett综合征中的长链脂肪酸。 Very long-chain fatty acids in Rett syndrome. |
| 已发布 PubMed:氰基甲基化后气相色谱-氮-磷检测测定血清中的长链脂肪酸。 Determination of very-long-chain fatty acids in serum by gas chromatography-nitrogen-phosphorus detection following cyanomethylation. |
| 已发布 PubMed:3中血浆超长链脂肪酸 Plasma very long chain fatty acids in 3,000名过氧化物酶血症患者和29名 000 peroxisome disease patients and 29,000个控件。 000 controls. |
| 已发布 PubMed:一种基于hplc的新方法，用于定量分析内部角质层脂质，并特别提及游离脂肪酸组分。 A new HPLC-based method for the quantitative analysis of inner stratum corneum lipids with special reference to the free fatty acid fraction. |
| 已发布 PubMed:异烟肼对结核分枝杆菌β-酮酰基acp合酶的抑制作用 Inhibition of a Mycobacterium tuberculosis beta-ketoacyl ACP synthase by isoniazid. |
| 已发布 PubMed:醇患者的红细胞膜超长链脂肪酸异常 Abnormality of very long-chain fatty acids of erythrocyte membrane in alcoholic patients. |
| 已发布 PubMed:气相色谱脂肪酸和分支杆菌酸裂解产物的测定可区分Genavense的分枝杆菌 Use of gas chromatographic fatty acid and mycolic acid cleavage product determination to differentiate among Mycobacterium genavense, 福特分枝杆菌 Mycobacterium fortuitum, 西米分枝杆菌 Mycobacterium simiae, 和结核分枝杆菌。 and Mycobacterium tuberculosis. |
| 已发布 PubMed:增加铜蓝蛋白血症患者红细胞膜中的长链脂肪酸。 Increased very long-chain fatty acids in erythrocyte membranes of patients with aceruloplasminemia. |
| 已发布 PubMed:双胞胎新生儿中一种新的过氧化物酶体β-氧化疾病 A new peroxisomal beta-oxidation disorder in twin neonates: cerotic和原始的 pristanic酸氧化不良。 |
| 已发布 PubMed:十六烷酸对断奶和断奶后大鼠生化髓鞘组成的影响 Effects of exogenous hexacosanoic acid on biochemical myelin composition in weaning and post-weaning rats. |
| 已发布 PubMed:神户地震中挤压综合征患者的超长链脂肪酸模式。 Very long-chain fatty acid pattern in crush syndrome patients in the Kobe earthquake. |
| 已发布 PubMed:X联肾上腺皮质营养不良症中的血浆磷脂脂肪酸。 Plasma phospholipid fatty acids in X-linked adrenoleukodystrophy. |
| 已发布 PubMed:长链脂肪酸与模型膜和血清白蛋白的相互作用对肾上腺白质营养不良的发病机制的影响。 Interactions of a very long chain fatty acid with model membranes and serum albumin. Implications for the pathogenesis of adrenoleukodystrophy. |
| 已发布 PubMed:布氏分枝杆菌十一月 Mycobacterium branderi sp. nov., 一种新的潜在 类病原体。 a new potential human pathogen. |
| 已发布 PubMed:培养的 皮肤成纤维细胞中过氧化物酶体脂肪酸β-氧化的检测 Measurement of peroxisomal fatty acid beta-oxidation in cultured human skin fibroblasts. |
| 已发布 PubMed:X联肾上腺皮质营养不良的饮食管理。 Dietary management of X-linked adrenoleukodystrophy. |
| 已发布 PubMed:培养的 皮肤成纤维细胞中脂肪酸β-氧化缺乏氧化磷酸化的能力。 Beta-oxidation of fatty acids in cultured human skin fibroblasts devoid of the capacity for oxidative phosphorylation. |
| 已发布 PubMed:血浆中超长链脂肪酸分布 Profiles of very-long-chain fatty acids in plasma, 成纤维细胞 fibroblasts, 氏综合征中的血液和血细胞 and blood cells in Zellweger syndrome, X连锁肾上腺白质营养不良 X-linked adrenoleukodystrophy, 和根状软骨发育不良。 and rhizomelic chondrodysplasia punctata. |
| 已发布 PubMed:非诺洛芬对大鼠肝脏肝细胞和亚细胞级分中长链和超长链脂肪酸活化和氧化作用的研究。 Studies on the effect of fenoprofen on the activation and oxidation of long chain and very long chain fatty acids in hepatocytes and subcellular fractions from rat liver. |
| 已发布 PubMed:分枝杆菌十一月 Mycobacterium celatum sp. nov. |
| 已发布 PubMed:拟南芥中t-dna插入诱导的cereriferum（cer）突变体的分离和鉴定。 Isolation and characterization of eceriferum (cer) mutants induced by T-DNA insertions in Arabidopsis thaliana. |
| 已发布 PubMed:在大鼠实验性增加血清超长链脂肪酸影响下改变了肾上腺皮质反应。 Altered adrenocortical response under the influence of experimentally increased serum very long chain fatty acids in rats. |
| 已发布 PubMed:正常和过氧化物酶体缺乏（zellweger）成纤维细胞中由[2-14c]乙酸盐合成脂肪酸。 Fatty acid synthesis from [2-14C]acetate in normal and peroxisome-deficient (Zellweger) fibroblasts. |
| 已发布 PubMed:诊断与橙花系统疾病有关的过氧化物酶体异常。 Diagnosis of peroxisomal disorders with neurological involvement. |
| 已发布 PubMed:通过生化测试和脂质分析表征一组缓慢增长的分枝杆菌。 Characterization of a distinct group of slowly growing mycobacteria by biochemical tests and lipid analyses. |
| 已发布 PubMed:用高剂量吩噻嗪或噻吨蒽治疗的精神分裂症患者的血小板中缺乏多不饱和脂肪酸。 Schizophrenic patients treated with high dose phenothiazine or thioxanthene become deficient in polyunsaturated fatty acids in their thrombocytes. |
| 已发布 PubMed:X联肾上腺皮质营养不良症白质中的磷脂 Phospholipids in X-linked adrenoleukodystrophy white matter: 脱髓鞘发作前出现脂肪酸异常。 fatty acid abnormalities before the onset of demyelination. |
| 已发布 PubMed:患有过氧化物酶体β-氧化缺陷的男婴的新生儿癫痫发作和严重的肌张力降低。 Neonatal seizures and severe hypotonia in a male infant suffering from a defect in peroxisomal beta-oxidation. |
| 已发布 PubMed:大鼠脑中超长链脂肪酸氧化 Oxidation of very-long-chain fatty acids in rat brain: 芥酸 cerotic acid仅在大鼠脑过氧化物酶体中被β氧化。 |
| 已发布 PubMed:有确凿证据表明，超长链脂肪酸仅在 皮肤成纤维细胞的过氧化物酶体中氧化。 Conclusive evidence that very-long-chain fatty acids are oxidized exclusively in peroxisomes in human skin fibroblasts. |
| 已发布 PubMed:大鼠肝脏过氧化物酶体和微粒体中的长链酰基辅酶A合成酶和超长链酰基辅酶A合成酶活性。酶学研究。 Long-chain-acyl-CoA synthetase and very-long-chain-acyl-CoA synthetase activities in peroxisomes and microsomes from rat liver. An enzymological study. |
| 已发布 PubMed:毛果天花粉的果皮化学成分的危害 [Chemical constituents of the pericarp of Trichosanthes rosthornii Harms]. |
| 已发布 PubMed:简化的气相色谱-质谱法测定血浆中的长链脂肪酸 Determination of very-long-chain fatty acids in plasma by a simplified gas chromatographic-mass spectrometric procedure. |
| 已发布 PubMed:中枢橙花系统畸形和假性新生儿肾上腺白质营养不良的白质改变。 Central nervous system malformations and white matter changes in pseudo-neonatal adrenoleukodystrophy. |
| 已发布 PubMed:婴儿植酸贮积病 Infantile phytanic acid storage disease, 过氧化物酶体生物发生障碍 a disorder of peroxisome biogenesis: 病例报告。 a case report. |
| 已发布 PubMed:肾上腺橙花病 Adrenomyeloneuropathy 呈现 presenting as Addison's 疾病 disease in 童年 childhood. |
| 已发布 PubMed:饮食芥酸疗法用于X联肾上腺皮质营养不良。 Dietary erucic acid therapy for X-linked adrenoleukodystrophy. |
| 已发布 PubMed:分枝杆菌脂肪酸和醇的气相色谱 Gas chromatography of mycobacterial fatty acids and alcohols: 诊断应用程序。 diagnostic applications. |
| 已发布 PubMed:霉菌酸裂解产物的毛细管气相色谱分析 Capillary gas chromatographic analysis of mycolic acid cleavage products, 细胞脂肪酸 cellular fatty acids, 和异种分枝杆菌的醇。 and alcohols of Mycobacterium xenopi. |
| 已发布 PubMed:植酸 Phytanic acid, 黄烷酸 pristanic acid, 毛细管气相色谱法同时测定超长链脂肪酸甲酯 and very-long-chain fatty acid methyl esters measured simultaneously by capillary gas chromatography. |
| 已发布 PubMed:肾上腺皮质营养不良中红细胞膜磷脂中的长链脂肪酸含量很高。 Very long-chain fatty acids in erythrocyte membrane phospholipids in adrenoleukodystrophy. |
| 已发布 PubMed:日本常见食品中己酸含量。 Hexacosanoate contents in Japanese common foods. |
| 已发布 PubMed:[两个成年 的肾上腺白质营养不良症的临床特征为纹状体黑质变性-一种可能是肾上腺白质营养不良的变体]。 [Two adult cases of adrenoleukodystrophy with clinical features of striatonigral degeneration--a probable variant of adrenoleukodystrophy]. |
| 已发布 PubMed:过氧化物酶体激活x连锁肾上腺皮质营养不良症中超长链脂肪酸能力受损。 Impaired ability of peroxisomes to activate very-long-chain fatty acids in X-linked adrenoleukodystrophy. |
| 已发布 PubMed:直接证明在X链肾上腺皮质营养不良中非常长链脂肪酸氧化不足是由于过氧化物酶体激活非常长链脂肪酸能力受损所致。 Direct demonstration that the deficient oxidation of very long chain fatty acids in X-linked adrenoleukodystrophy is due to an impaired ability of peroxisomes to activate very long chain fatty acids. |
| 已发布 PubMed:高效液相色谱法检测肾上腺皮质营养不良的携带者。 Carrier detection for adrenoleukodystrophy by high-performance liquid chromatography. |
| 已发布 PubMed:修饰对半合成脑苷硫酸盐相行为的影响。 Influence of structural modifications on the phase behavior of semi-synthetic cerebroside sulfate. |
| 已发布 PubMed:婴幼儿植酸储存病的治疗 Treatment of infantile phytanic acid storage disease: 临床 clinical, 治疗2年的两个孩子的生化和超微结构发现。 biochemical and ultrastructural findings in two children treated for 2 years. |
| 已发布 PubMed:长链的影响 Effects of long-chain, 饱和脂肪酸对 肾上腺皮质细胞膜微粘度和促肾上腺皮质激素反应性的影响。 saturated fatty acids on membrane microviscosity and adrenocorticotropin responsiveness of human adrenocortical cells in vitro. |
| 已发布 PubMed:过氧化物酶体脂肪酸β-氧化与zellweger综合征和其他过氧化物酶体疾病患者培养的皮肤成纤维细胞中非常长链脂肪酸积累有关。 Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders. |
| 已发布 PubMed:大鼠肝脏线粒体和过氧化物酶体的长链脂肪酸β-氧化。 Very long chain fatty acid beta-oxidation by rat liver mitochondria and peroxisomes. |
| 已发布 PubMed:通过测量长链脂肪酸（c26）进行zellweger综合征的产前诊断 Prenatal diagnosis of Zellweger syndrome by measurement of very long chain fatty acid (C26:0）培养的绒毛膜绒毛成纤维细胞中的β-氧化 0) beta-oxidation in cultured chorionic villous fibroblasts: 对其他过氧化物酶体疾病的早期诊断具有重要意义。 implications for early diagnosis of other peroxisomal disorders. |
| 已发布 PubMed:肾黏膜明串球菌营养不良的活检直肠粘膜的电镜研究。 Electronmicroscopic study on biopsied rectal mucosa in adrenoleukodystrophy. |
| 已发布 PubMed: 皮肤成纤维细胞对超长链脂肪酸及其辅酶α衍生物的β-氧化作用。 Beta-oxidation of very-long-chain fatty acids and their coenzyme A derivatives by human skin fibroblasts. |
| 已发布 PubMed:肾上腺白质营养不良 Adrenoleukodystrophy: 从床旁到分子生物学。 from bedside to molecular biology. |
| 已发布 PubMed:肾上腺白质营养不良 Adrenoleukodystrophy: 日粮油酸降低了己酸含量。 dietary oleic acid lowers hexacosanoate levels. |
| 已发布 PubMed:肾上腺橙花营养不良的新型饮食疗法 A new dietary therapy for adrenoleukodystrophy: 生化和初步临床结果36例。 biochemical and preliminary clinical results in 36 patients. |
| 已发布 PubMed:肾上腺白质营养不良 Adrenoleukodystrophy: 诊断中的生化程序 biochemical procedures in diagnosis, 预防和治疗。 prevention and treatment. |
| 已发布 PubMed:一种使用滤纸上的干血斑诊断肾上腺皮质营养不良的简单方法。 A simple method to diagnose adrenoleukodystrophy using a dried blood spot on filter paper. |
| 已发布 PubMed:肾上腺白质营养不良。肾上腺髓质脊髓橙花病尸检病例报告。 Adrenoleukodystrophy. Report of an autopsy case with adrenoleukomyeloneuropathy. |
| 已发布 PubMed:红细胞膜鞘磷脂中的长链脂肪酸 Very long-chain fatty acids in erythrocyte membrane sphingomyelin: 检测醛半合子和杂合子。 detection of ALD hemizygotes and heterozygotes. |
| 已发布 PubMed:毛细管气相色谱法分析分枝杆菌物种的分枝杆菌酸裂解产物和细胞脂肪酸 Analysis of mycolic acid cleavage products and cellular fatty acids of Mycobacterium species by capillary gas chromatography. |
| 已发布 PubMed:肾上腺白质营养不良 Adrenoleukodystrophy: 油酸降低成纤维细胞饱和的c22-26脂肪酸。 oleic acid lowers fibroblast saturated C22-26 fatty acids. |
| 已发布 PubMed:代谢[17 Metabolism of [17,18-3h2]己酸和[15 18-3H2]hexacosanoic acid and [15,16-3h2]来自肾上腺皮质营养不良（ald）和肾上腺皮质橙花病（amn）患者的培养皮肤成纤维细胞中的木质酸。 16-3H2]lignoceric acid in cultured skin fibroblasts from patients with adrenoleukodystrophy (ALD) and adrenomyeloneuropathy (AMN). |
| 已发布 PubMed:肾上腺皮质营养不良培养的皮肤成纤维细胞的中性脂质和甘油磷脂中的长链脂肪酸。 Very long-chain fatty acids in neutral lipids and glycerophospholipids of adrenoleukodystrophy-cultured skin fibroblasts. |
| 已发布 PubMed:[肾上腺皮质橙花病的心电图和诱发电位]。 [EMG and evoked potentials in adrenomyeloneuropathy]. |
| 已发布 PubMed:没有肾上腺功能不全的肾上腺白质营养不良及其磁共振成像。 Adrenoleukodystrophy without adrenal insufficiency and its magnetic resonance imaging. |
| 已发布 PubMed:不安 Disturbed 非常 very 长 long 链 chain (C24-C26) 脂肪的 fatty acid 图案 pattern in 成纤维细胞 fibroblasts of 耐心 patients with Zellweger Zellweger's 综合症 syndrome. |
| 已发布 PubMed:通过确定非常长的链脂肪酸水平并通过与dna探针的连锁分析，可以在孕早期对肾上腺白质营养不良进行产前诊断。 First trimester prenatal diagnosis of adrenoleukodystrophy by determination of very long chain fatty acid levels and by linkage analysis to a DNA probe. |
| 已发布 PubMed:家族性肾上腺橙花营养不良一例的成 披露。 [Adult disclosure of a case of familial adrenoleukodystrophy]. |
| 已发布 PubMed:反相色谱法测定c20-c30脂肪酸 Determination of C20-C30 fatty acids by reversed-phase chromatographic techniques: 一种定量分析肾上腺白质营养不良患者血清中微量脂肪酸有效方法。 an efficient method to quantitate minor fatty acids in serum of patients with adrenoleukodystrophy. |
| 已发布 PubMed:等离子体 Plasma and skin 皮 成纤维细胞 fibroblasts C26 脂肪的 fatty acids acids in 婴儿的 婴儿 infantile Refsum's 疾病 disease. |
| 已发布 PubMed:限制在饱和超长链脂肪酸中的饮食设计 The design of a diet restricted in saturated very long-chain fatty acids: 在肾上腺橙花营养不良中的治疗应用。 therapeutic application in adrenoleukodystrophy. |
| 已发布 PubMed:临床诊断为两个兄弟的肾上腺皮质营养不良的生化证据。 Biochemical evidence for clinically diagnosed adrenoleucodystrophy in two brothers. |
| 已发布 PubMed:脑肝肾综合征（zellweger）。超长链脂肪酸水平升高和受损的减弱以及它们在产前诊断中的用途。 The cerebrohepatorenal (Zellweger) syndrome. Increased levels and impaired degradation of very-long-chain fatty acids and their use in prenatal diagnosis. |
| 已发布 PubMed: Zellweger Zellweger综合征患者血清中很长链脂肪酸模式。 |
| 已发布 PubMed:肾上腺橙花营养不良的产前诊断。在培养的羊膜细胞和胎儿肾上腺中增加十六烷酸水平的证据。 The prenatal diagnosis of adrenoleukodystrophy. Demonstration of increased hexacosanoic acid levels in cultured amniocytes and fetal adrenal gland. |
| 已发布 PubMed:己二十烷酸（c23 Increased synthesis of hexacosanoic acid (C23:0）通过培养患有肾上腺白质营养不良（ald）和肾上腺髓质性橙花病（amn）的患者的皮肤成纤维细胞。 0) by cultured skin fibroblasts from patients with adrenoleukodystrophy (ALD) and adrenomyeloneuropathy (AMN). |
| 已发布 PubMed:肾上腺皮质营养不良患者红细胞膜鞘磷脂中长链脂肪酸异常 Abnormality of long-chain fatty acids in erythrocyte membrane sphingomyelin from patients with adrenoleukodystrophy. |
| 已发布 PubMed: 和大鼠脑胆固醇酯酶对长链脂肪酸代谢的特异性 Specificities of human and rat brain enzymes of cholesterol ester metabolism toward very long chain fatty acids: 对肾上腺白质营养不良的生化发病机制的影响。 implication for biochemical pathogenesis of adrenoleukodystrophy. |
| 已发布 PubMed:大脑中的脂肪酸模式 Fatty acid patterns in brain, 成纤维细胞 fibroblasts, 肾上腺白质营养不良中的明串球菌和体液脂质。 leukocyte and body fluid lipids in adrenoleukodystrophy. |
| 已发布 PubMed:肾上腺白质营养不良 Adrenoleukodystrophy: 有证据表明脑胆固醇酯的异常极长链脂肪酸是外源性的。 evidence that abnormal very long chain fatty acids of brain cholesterol esters are of exogenous origin. |
| 已发布 PubMed:肾上腺白质营养不良 Adrenoleukodystrophy: 培养的皮肤成纤维细胞中c26脂肪酸含量升高。 elevated C26 fatty acid in cultured skin fibroblasts. |
| 已发布 PubMed: 亚普雷尼斯 yapurenis（euophorbiaceae）的成分。 |
| 已发布 PubMed:肾上腺白质营养不良的代谢研究。 Metabolic studies of adrenoleukodystrophy. |
3D/INCHI